- Case Report
- A Case of Gaucher's Disease.
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J S Kim, S J Kim, H J Suh, I J Kang, S Y Chung, J B Park, S K Moon, S Y Kim
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Clin Exp Pediatr. 1986;29(9):1028-1034. Published online September 30, 1986
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We experienced a case of adult type Gaucher's disease in 14 month old male.
The patient showed hepatosplenomegaly with anemia and characteristic Gaucher cells in bone marrow aspiration and biopsy of liver and spleen both in light microscopic and electromicroscopic examination. Splenectomy was followed by improvement of anemia and thrombocytopenia but hepatomegaly remained even progressed.
A brief review of literature was... |
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- A case of Letterer-Siwe disease.
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H J Suh, E H Kang, K C Han, S K Moon
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Clin Exp Pediatr. 1982;25(9):954-958. Published online September 30, 1982
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A case of Letterer-Siwe disease in a 2 year old boy manifesting such classic signs described
by Siwe as, hepatosplenome^aly, swelling of lymph node, bleeding tendency, anemia, fever
and bony skull defects is presented.
The diagnosis was confirmed by clinical symptoms, laboratory data, histopathologic and
radiologic fingings.
The authors report a fatal case which was treated in this hospital with review of pertinent
literatures.
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