- Case Report
- A Case of Congenital Hepatic Fibrosis Accompanied by
Renal Tubular Ectasia, Caroli Syndrome and Choledochal Cyst
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Bong Seok Choi, Sang Nam Bae, Yong Tak Im, Jae Hong Park, Chang Hoon Lee, Jun Woo Lee
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Clin Exp Pediatr. 2002;45(7):923-927. Published online July 15, 2002
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Congenital hepatic fibrosis is a relatively rare disease, characterized by bile ductular proliferation and prominent fibrosis in the portal area of liver resulting in portal hypertension. It is frequently associated with other abnormalities such as polycystic kidney, Caroli syndrome, cystic dysplasia of pancreas, intestinal lymphangiectasia, pulmonary emphysema, hemangioma, and cleft palate. We report here a case of congenital hepatic fibrosis... |
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