- Original Article
- Sodium and calcium transport in spherocytic red blood cells.
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Shin Heh Kang, Kir Young Kim, Young Ho Lee, Bok Soon Kang
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Clin Exp Pediatr. 1991;34(7):978-991. Published online July 31, 1991
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Hereditary spherocytosis (HS) is an autosomal, dominantly inherited hemolytic disorder which
shows characteristic spherocytes on peripheral smear. As spherocytes are rounder, more fragile and
susceptible to extravascular hemolysis in the spleen, HS patients suffer from variable degrees of
anemia, jaundice, splenomegaly and gall stones. However the pathogenesis is heterogenous in HS,
such as spectrin deficiency, decreased spectrin-protein 4.1 binding, increased spectrin binding to the
RBC... |
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- A Case of 9p-Syndrome.
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Bok Hoi Kim, Shin Heh Kang, Kir Young Kim, Kyung Ja Cho, Kyung Hee Ha, Bum Suk Lee
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Clin Exp Pediatr. 1990;33(9):1262-1265. Published online September 30, 1990
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We experienced a case of 9p- syndrome in a 2 year and 5 month old male child who manifested
psychomotor retardation and multiple congenital anomalies.
His karyotype was 46, XY, del (9) (p22).
A brief review of literature was also presented. |
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- Ultrasonographic Diagnosis of Congenital Hypertrophic Pyloric Stenosis.
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Shin Heh Kang, Chul Lee, Ran Namgung, Dong Gwan Han, Ki Keun Oh, Seung Hun Choi
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Clin Exp Pediatr. 1989;32(6):756-764. Published online June 30, 1989
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The diagnosis of congenital hypertrophic pyloric stenosis has traditionally been made on the basis
of history and physical examination in the majority of patients. Imaging procedures such as UGI
series have been reserved for vomiting infats in whom the diagnosis was obscure. More recently
ultrasonography with the lack of hazards associated with radiation provides an additional method of
investigation which is accurate and diagnose... |
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- A Clinical Study and Comprehensive Total Care in Hemophilia.
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Shin Heh Kang, Chang Hyun Yang, Kir Young Kim
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Clin Exp Pediatr. 1988;31(2):202-211. Published online February 28, 1988
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Hemophilia is one of the hereditary coagulation disorders characterized by deficiency in plasma
clotting facotrs such as factor VIII and IX. As life long bleeding occurs in hemophiliacs, continous
comprehensive total care is required for the patients. After the self therapy, home care program was
introduced in the 1970s’ in the United States, there was significant reduction in absentism, hospitalized
days, outpatient visits, decrease... |
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- 2 Cases of Infantile Spasms(Cryptogenic Type) Treated with ACTH Therapy.
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Shin Heh Kang, Chang Jun Coe
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Clin Exp Pediatr. 1987;30(8):928-933. Published online August 31, 1987
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We have experienced 2 cases of infantile spasms treated with ACTH. They were diagnosed as
cryptogenic type within relatively short duration after the onset. With the administration of ACTH,
flexor spasms and hypsarrhythmia disappeared. They did not demonstrate any intellectual impair-
ment on OPD follow up study. A brief review of literatures was made.
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- Case Report
- A Case of Renal Candidiasis Associated with Type I Diabetes Mellitus.
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Shin Heh Kang, Jae Seung Lee, Duk Hi Kim
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Clin Exp Pediatr. 1987;30(6):677-683. Published online June 30, 1987
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We have experienced a case of renal candidiasis in type I DM (IDDM). The patient was a 15-year old girl
who suffered from type I DM since 3 years earlier with development of retinopathy,
cataract & renal failure. Ultrasonic examination revealed multiple fungus balls in renal pelvis & urinary bladder. Candida tropicalis was cultured from fungus balls passed during urination.
A brief... |
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- A case of Unilateral Absence of Pulmonary Artery.
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Kwang Sin Joh, Dong Soo Kim, Chul Joo Ryu, Shin Heh Kang, Sung Kyu Lee, Ki Young Lee, Dong Shik Chin
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Clin Exp Pediatr. 1986;29(5):559-563. Published online May 31, 1986
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Unilateral Absence of Pulmonary Artery(UAPA) is a rare disease. It is characterized by no specfiic cardiopulmonary symptoms in general. We experienced a case of UAPA in a 9 year-old female patient with the chief complaint of abnormal chest Xray finding. Lung perfusion scan, cardiac catheterization with pulmonary and aortic angiography confirmed the diagnosis of right side UAPA.
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