- Case Report
- Oncology
- Targeted busulfan and fludarabine-based conditioning for bone marrow transplantation in chronic granulomatous disease
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Hee Young Ju, Hyoung Jin Kang, Che Ry Hong, Ji Won Lee, Hyery Kim, Sang Hoon Song, Kyung-Sang Yu, In-Jin Jang, June Dong Park, Kyung Duk Park, Hee Young Shin, Joong-Gon Kim, Hyo Seop Ahn
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Clin Exp Pediatr. 2016;59(Suppl 1):S57-S59. Published online November 30, 2016
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Chronic granulomatous disease (CGD) is a primary immunodeficiency disease caused by impaired phagocytic function. Hematopoietic stem cell transplantation (HSCT) is a definitive cure for CGD; however, the use of HSCT is limited because of associated problems, including transplantation-related mortality and engraftment failure. We report a case of a patient with CGD who underwent successful HSCT following a targeted busulfan and... |
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- Review Article
- Pathogenesis and clinical manifestations of juvenile rheumatoid arthritis
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Youn-Soo Hahn, Joong-Gon Kim
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Clin Exp Pediatr. 2010;53(11):921-930. Published online November 30, 2010
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Juvenile rheumatoid arthritis (JRA) is the most common rheumatic childhood disease; its onset is before 16 years of age and it persists for at least 6 weeks. JRA encompasses a heterogeneous group of diseases that is classified according to 3 major presentations: oligoarthritis, polyarthritis, and systemic onset diseases. These presentations may originate from the same or different causes that involve... |
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- Case Report
- A Case of Common Variable Immunodeficiency with Autoimmune Hemolytic Anemia
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Kyung-Yil Lee, Yon-Joo Lee, Sang-Won Cha, Dong Joon Lee, Ji-Whan Han, Kyung-Tae Whang, Joong-Gon Kim
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Clin Exp Pediatr. 2000;43(1):117-122. Published online January 15, 2000
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Common variable immunodeficiency(CVID) is a heterogeneous collection of disorders with hypogammaglobulinemia
with recurrent bacterial infections and high incidence of autoimmune disorders
as its hallmark. We report a 7-year-old girl suffering from CVID with Coombs' test positive
hemolytic anemia. She had been relatively well until 23-months old when she was admitted to
Taejon St. Mary' s Hospital with pneumonia 5 years ago. Afterwards, she had... |
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