- Case Report
- Adrenaogenital Syndrome with Congenital Adrenal Hyperplasia.
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Kyeong Rae Moon, Yeong Bong Park, Sang Gi Kim, Jin Heon Kim, Chang Soo Ra, Jae Hong Seo, Ho Won Hwang
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Clin Exp Pediatr. 1985;28(1):78-84. Published online January 31, 1985
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Adrenogenital syndrome is caused by a defect in biosynthesis of adrenal corticoids as a result of deficiency in one of the essential enzymes, most commonly 21-hydroxylase. About 50% of 21-hydroxylase deficiency have salt losing type as a result of aldosterone deficiency. We have experienced a casa of adrenogenital syndrome associated with congenital adrenal hyperplasia (salt losing form) in a 3... |
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