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Case Report
Cases of Omental Cyst
Ju Seok Maeng, Hae Kyung Lee, Jae Ock Park, Sang Jhoo Lee, Chul Moon, Dong Wha Lee
Clin Exp Pediatr. 1992;35(1):129-134.   Published online January 15, 1992
A 3-year-old female patient was admitted due to marked abdomainal distension. Her mother has been noticed the abdominal distension since birth, and the abdomen was enlarged progressively, but there were no subjective symptoms such as abdominal pain, vomiting nor indigestion. The radiographic findings showed huge intraabdomainal mass anterior to intestine which had septated fluid collection in it. Omental cyst was...
Original Article
A Case of Type A Niemann-Pick Disease.
Young Bong Moon, Yang Bin Im, Dong Hwan Lee, Sang Jhoo Lee, In Sook Kim, Tae Jung Kwon, Dong Wha Lee
Clin Exp Pediatr. 1989;32(3):402-411.   Published online March 31, 1989
We experienced a case of type A Niemann-Pick disease in 31 month-old female infant. She showed dyspnea, marked hepatosplenomegaly and developmental retardation. Fundoscopic examination revealed cherry red spots in both macula. Autopsy finding revealed that Iiver, spleen, lung, kidney, bone marrow, lymph node and brain were involved. Especially multiple ischemic necrosis were found on cerebral and cerebellar white matter. Generalized muscular atrophy and reticular...
Case Report
A Case of Congenital Adrenal Agenesis.
Kyeong Wha Lee, Hyung Jin Choi, Sang Man Shin, Sang Jhoo Lee, Dong Wha Lee
Clin Exp Pediatr. 1984;27(11):1118-1122.   Published online November 30, 1984
Congenital adrenal agenesis or hypoplasia is very rare disorder which causes adrenal insufficiency. It is usually the result of an isolated defect of organogenesis. It may be sporadic, or it may express itself as an autosomal recessive or X-linked disorder within families. We experienced a baby who revealed hyperpigmentation, hypoglycemia, hyperkalemia and hyponatremia immediately after birth. Hormone study was compatible with primary adrenal insufficiency. Complete...
Two Cases of Late Infantile Metachromatic Leukodystrophy.
Mee Ran Roh, Kyeong Wha Lee, Dong Whan Lee, Sang Jhoo Lee, Dong Wha Lee, Duk Yong Kang, Tae Jung Kwon, Jung Sook Kim
Clin Exp Pediatr. 1984;27(10):1033-1039.   Published online October 31, 1984
Metachromatic leukodystrophy, a group of progressive degenerative neurologic disease with variable age of onset characterized by an autosomal recessive mode of inheritance, shows an accumulation of the sphingolipid, sulfatide, particularly in the Schwann cell of the central and peripheral nervous system by arysulfatase A deficiency. 2 cases of late infantile metachromatic leukodystrophy are reported, who developed normally during a infantile period,...
A Case of Dysplastic Kidney and Hydroureter with Distal Treterl Atresia.
Eun Mi Kim, Jei Hoon Yoo, Dong Whan Lee, Sang Jhoo Lee, Dong Wha Lee, Deuk Yong Kang
Clin Exp Pediatr. 1983;26(12):1254-1258.   Published online December 31, 1983
We presented a case of dysplastic kidney and Hydroureter with distal ureteral atresia and reviewed the literatures. This 5 year old male patient with abdominal mass for 3 years was admitted and took explo-laparotomy. The diagnosis was confirmed by explo-laparotomy and microscopic finding. Characteristic microscopic findings of dyaplastic kidney on present case are; 1) Primitive duct, ductules and glomeruli. 2) Duct was lined by cuboidal or columnar...
A Case of Diabetes Insipidus associated with Suprasellar Germinoma.
Soo Ok Lee, Hye Yung Hwang, Woo Hyun, Sang Jhoo Lee, Dong Wha Lee
Clin Exp Pediatr. 1980;23(12):1048-1053.   Published online December 15, 1980
We report I case of diabetes insipidus associated with suprasellar germinoma, obstructive hydrocephalus and both optic nerve atrophy. In this patient, symptoms of increased intracranial pressure was preceded by characteristic polyuria and polydipsia. The water restriction and pitressin test resulted in central originated diabetes insipidus. Computerized tomography in the brain revealed smooth marginated rounded mass density measuring 3.9 cm obliterating...
Histiocytic Medullary Reticulosis: A case record and literatures review.
Kwang Ho Kim, Chi Ok Ahn, Byoung Soo Kim, Kir Young Kim, Dong Wha Lee, In Joon Choi
Clin Exp Pediatr. 1978;21(5):403-411.   Published online May 31, 1978
Histiocytic medullary reticulosis was first described as a clinical and pathological entity by Scott and Robb-Smith in 1939. The clinical pictures include progressive pancytopenia, fever, wasting, lymphadenopathy, hepatosplenomegaly, jaundice and purpura. The outstanding morphological features of the disease is proliferation of histiocytes throughout the reticuloendothelial system with frequent leucoerythrophagocytosis. In spite of uniform clinical and fistologcal pictures verified by additional...
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