Journal of the Korean Pediatric Society 1980;23(4):321-325.
Published online April 15, 1980.
A Case of Nephrotic Syndrome Associated with Distal Type Tubular Acidosis, Nephrocalcinosis and Renal Osteodystrophy.
Young Mo Sohn1, Pyung Kil Kim1, In Joon Choi2, Chang Yun Park3
1Department of Pediatrics, College of Medicine Yonsei University, Seoul, Korea.
2Department of Pathology, College of Medicine Yonsei University, Seoul, Korea.
3Department of Radiology, College of Medicine Yonset University, Seoul, Korea.
원위 신세뇨관 산혈증과 신석회화증이 동반된 신증후군 1 예
손영모1, 김병길1, 최인준2, 박창윤3
1연세대학교 의과대학 소아과학교실
2연세대학교 의과대학 병리학교실
3연세대학교 의과대학 방사선과학교실
Abstract
A non-familial type nephrotic syndrome associated with distal renal tubual acidosis, nephrocalcinosis and renal osteodystropy is a very rare disease. A 4 year old boy was treated with prednisone under the impression of minimal lesion nephrotid syndrome but the response was not excellent along with persistant microhematuria in his serial urinalysis. Percutaneous renal biopsy speciman revealed microcalcification around afferent arteriols and peritubular area along with mild mesangial cell proliferations. Futher studies disclosed osteodystrophic change of the femurs. Patient had a typical forms of distal type renal tubular acidosis which was confirmed by NH4Cl and NaHCO3 loading tests. This case is the first cases of non-familial type nephrotic syndrome associated with nephrocalcinosis, renal osteodystrophy and distal RTA in Korea.




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