| Supraventricular tachycardia in a neonate with
cardiac rhabdomyoma and tuberous sclerosis |
|
In Kug Bang, Yeo Hyang Kim, Chun Soo Kim, Sang Lak Lee, Tae Chan Kwon |
|
Department of Pediatrics, School of Medicine, Keimyung University, Daegu, Korea |
| 상심실성 빈맥과 심장 종양으로 진단된 결절성 경화증 1예 |
|
방인국, 김여향, 김천수, 이상락, 권태찬 |
|
계명대학교 의과대학 소아과학교실 |
Correspondence:
Yeo Hyang Kim, Email: kimyhped@hanmail.net
|
|
|
|
|
| Abstract |
|
Primary tumors of the heart are uncommon among pediatric patients. Rhabdomyoma is the most frequent cardiac tumor in infants and children, which is commonly associated with tuberous sclerosis. Tuberous sclerosis is a neurocutaneous syndrome affecting the brain, heart, skin, and other organs. Cardiac rhadomyomas are reported in 50-64% of infants with tuberous sclerosis. Tuberous sclerosis involves multiple locations in the atrium, ventricle and septum, and may induce mechanical obstruction of the outflow tract and heart failure depending on the location, number, size, and degree of invasion of tumors. Arrhythmias may also develop in infants with cardiac rhadomyomas, but only a few of these patients require prolonged anti-arrhythmic therapy because arrhythmia often disappears with spontaneous regression of the tumors, and the ultimate prognosis may be decided by the cerebral manifestations. |
| Key Words:
Tuberous sclerosis, Rhabdomyoma, Arrhythmia |
|
PDF Links
Download Citation
