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A Clinical Study of Interrupted Aortic Arch

Journal of the Korean Pediatric Society 1995;38(10):1349-1355.
Published online October 15, 1995.
A Clinical Study of Interrupted Aortic Arch
Myoung Dong Shin1, Tae Hun Kang1, Hyoung Doo Lee1, Si Chan Sung2
1Department of Pediatrics, Dong-A University, College of Medicine, Pusan
2Department of Thoracic & Cardiovascular Surgery, Dong-A University, College of Medicine, Pusan
대동맥궁 중단(Interrupted Aortic Arch)의 임상적 고찰
신명동1, 강태훈1, 이형두1, 성시찬2
1동아대학교 의과대학 소아과학교실
2동아대학교 의과대학 흉부외과학교실
Abstract
Purpose
: We conducted this study to determine the clinical manifestations and prognostic factors of interrupted aortic arch(IAA).
Methods
: We performed retrospective clinical study with chart review in 9 infants who were diagnosed as IAA between January, 1993 and December, 1994.
Results
: Infants with IA were from 7 days to 92 days of age. Among them, 6 cases were type A, 3 cases were type B. PDA and VSD were seen in all infants with IAA and 2 cases of type B IAA were associated with Taussing-Bing anomaly. For the diagnostic method, 7 infants could be confirmed by echocardiography, so it seems to be relatively accurated diagnostic procedure. We tried PGE,1 in 6 patients with obvious clinical improvement. One of them, even in 53 days old case, there was responsed to PGE1. We attempted complete repair in 6 cases of IAA, 3 patients survived but one patient developed coarctation at anastomosis site, for which we performed balloon angioplasty successfully. With regard to survival rate of patients, for the cases who were diagnosed before 14 days old was 100%, but for the cases who were diagnosed after 14 days since birth, none survived.
Conclusion
: The survival rate in patients of IAA, depends mainly on early recognition and aggressive medical treatment before development of serious symptoms such as cardiogenic shock.
Key Words: Interrupted aortic arch, Balloon angioplasty


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