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Case Report
A Case of Letterer-Siwe Disease.
Suh Hong Ha, Jeong Sil Han, Sung Won Kim, Kyung Tae Kim, Kil Hyun Kim, Chung Hee Chi
Clin Exp Pediatr. 1987;30(3):335-341.   Published online March 31, 1987
Letterer-Siwe disease is a variant of Histiocytosis X and characterized by onset in infancy, hepatosplenomegaly, lymphadenopathy, bleeding tendency, hypochromic anemia, fever, localized bone defect and fatal outcome. The diagnosis was confirmed by clinical symptoms, laboratory datas, histopathologic and radiologic findings. We experienced a case which was treated by single prednisolone method and resulted to good response. A brief review of literature was made.
A case of Letterer-Siwe disease.
H J Suh, E H Kang, K C Han, S K Moon
Clin Exp Pediatr. 1982;25(9):954-958.   Published online September 30, 1982
A case of Letterer-Siwe disease in a 2 year old boy manifesting such classic signs described by Siwe as, hepatosplenome^aly, swelling of lymph node, bleeding tendency, anemia, fever and bony skull defects is presented. The diagnosis was confirmed by clinical symptoms, laboratory data, histopathologic and radiologic fingings. The authors report a fatal case which was treated in this hospital with review of pertinent literatures.
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