Journal of the Korean Pediatric Society 1967;10(3):159-164.
Published online March 31, 1967.
Progressive Muscular Dystrophy
Hae Sun Yoon, Young Soon Yoo, Churl Young Chung, Yun Hwa Kim
Department of Pediatrics,Catholic Medical College
進 行 性 筋 奏縮症 一4例報告와 文獻的 考察一 .
尹惠善, 柳寧順·, 鄭喆永, 金允華
가톨릭 醫大小兒科學敎室
Abstract
This paper presents the four cases of Progressive Muscular Dystrophy experienced during past one year from May 1965 to June 1966. All of them were male patients, their age were 7,10,15 and 7 years of age respectively and Case I and Case 2 were siblings. The four cases were classified clinically as Duchene Type of Muscular Dystrophy, but the Case 3 was much more resemble to the Fascio-Scapulo-Humoral Type (Landouzy and Dejerine Type). The creatin and creatinine ratio in urine was remarkably increased in all cases, the high titer o£ S.G.O.T. was demonstrated in one of them. The muscle biopsy findings showed the typical, advanced histological features in Case 3 and 4, and the others presented the mild histological changes compared with the clinical findings.




Close layer
prev next