A Case of Marfan's Syndrome. |
Ki Hyun Yoon, Jung Suh Suh, Son Sang Suh, Jong Woo Shin |
Department of Pediatrics, College of Medicine,Busan National University. |
Marfan 증후군 1례 |
윤기현, 서정서, 서손상, 신종우 |
부산대학교 의과대학 소아과학교실 |
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Abstract |
We have experinced a case of Marfan’s syndrome'in 27 months old female children. Marfan's syndrome is characterized by skeletal, ocular and cardiovascular abnormalities. Diagnosis was established by clinical characteristics with radiologic and laboratory findings. Pertiment literatures on Marfan’s syndrome also reviewed briefly.
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Key Words:
Marfan's syndrome, Dolichomorphism, Metacarpal index. |
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