| A Case of Congenital Nephrogenic Diabetes Insipidus. |
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Jae Sook Kim, Sook Hee Kong, Choong Hee Kim |
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Department of Pediatrics, National Seoul Hospital, Seoul，Korea |
| 선천성 신성뇨붕증 1례 |
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김재숙, 공숙희, 김충희 |
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국립서울병원 소아과 |
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| Abstract |
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This 18/12-year old female baby was diagnosed as primary nephrogenic diabetes insipidus，
whose main complaint was polydypsia and polyuria from birth, subsequently she developed failure to thrive.
Family history was nonspecific. Laboratory findings revealed failure of concentrates urine
with water restriction test and pitressin test. And so renal hypoplasia on the right side was revealed on retrograde pyelography and renal scan. She was treated with Indomethcin 2 mg/kg/day plus Chlorothiazide 500 mg/day and increased urine osmolarity, implying that endogenous prostaglandins may be modulators of renal sodium excretion.
She are doing well on the above mentioned regimens and no side effects have been observed after one year treatment.
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| Key Words:
Diabetes Insipidus, Nephrogenic, Congenital. |
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