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Adrenal Cortical Carcinoma in a Nineteen Month Old Girl.

Journal of the Korean Pediatric Society 1984;27(4):413-418.
Published online April 30, 1984.
Adrenal Cortical Carcinoma in a Nineteen Month Old Girl.
Sei Weon Yang, Jong Jin Seo, Hyung Ro Moon
Department of Pediatrics, College of Medicine, Seoul National University
소아부신피질 암종 1례
양세원, 서종진, 문형로
서울대학교 의과대학 소아과학교실
Abstract
Adrenal carcinoma is a rare disease both in adults and in children. Most of these tumors are functional, especially in children, producing endocrine syndromes such as Cushing syndrome, virilization, feminization or precocious puberty. The authors report a nineteen month old girl who exhibited features of Cushing syndrome and virilization caused by adrenal cortical carcinoma measuring 5.5X5.0X2.8 cm. She was successfully treated by total left adrenalectomy and has been followed up without problem over eight months.
Key Words: Adrenal cortical carcinoma, Cushing syndrome, Virilization


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