Journal of the Korean Pediatric Society 1985;28(6):616-621.
Published online June 30, 1985.
2 Cases of von Gierke's Disease.
Jeong Soo Park1, Ki Sup Chung1, Kwang Kil Lee2, In Joon Choi2
1Department of Pediatrics, College of Medicine, Yonsei University
2Department of Pathology, College of Medicine, Yonsei University
Von Gierke 씨 병 2례
박정수1, 정기섭1, 이광길2, 최인준2
1연세대학교 의과대학 소아과학교실
2연세대학교 의과대학 병리학 교실
Abstract
We have experienced 2 cases of glycogen storage disease who were clinically suspected of von Gierke’s disease. Each had a typical clinical findings of marked abdominal distension due to hepatosplenomegaly and also had a typical laboratory findings. Liver biopsy disclosed morphologic details of glycogen storage disease. The authors reported a von Gierke’s disease with a brief review of related literatures.
Key Words: von Gierke’s disease




Close layer
prev next