Journal of the Korean Pediatric Society 1987;30(3):314-319.
Published online March 31, 1987.
A Case of Distal Type of Renal Acidosis.
Han young Jeong, Soon Yol Whang, Sung Won Kim, Kyung Tae Kim, Kil Hyun Kim
Department of Pediatrics, St. Benedict Hospital, Busan, Korea
원위 신세뇨관 산혈증 1례
정한영, 황순열, 김성원, 김경태, 김길현
부산성분도병원 소아과
Abstract
A 5 years old girl was admitted to Ped. Dept, of St. Benedict Hospital due to pneumonia, gait disability and knock knee. Physical examination on admission showed a picture of full blown rickets such as poor development, waddling gait, knock knee, widening of both wrists, rachitic rosary and compatible X-ray picture. IVP showed bilateral nephrocalcinosis with normal excretory function. Laboratory data showed hypematremin, hyperchloremia, hypokalemia and high alkaline phosphatase level. Blood gas analysis showed severe metabolic acidosis In spite of these data, urine pH was above 6.0. Under the impression of renal tubular acidosis (distal type), alkali therapy with NaHCO3 and potassium supplement were done. After 2 weeks of treatment, marked improvement was noted both in clinical symptoms and laboratory results. With the review of literatures, the case is presented.
Key Words: Renal tubular acidosis, Distal type.




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