Journal of the Korean Pediatric Society 1988;31(3):398-403.
Published online March 31, 1988.
A Case of Kasabach-Merritt Syndrome.
S H Lee, S J Kim, H D Cha, T W Paik, C M Kang
Department of Pediatrics, Keimyung University, School of Medicine, Taegu, Korea
Kasabach-Merritt 증후군 1례
이순화, 김선진, 차홍대, 백태원, 강진무
계명대학교 의과대학 소아과학교실
Received: 18 November 1987
Abstract
Kasabach-Merritt syndrome (Giant hemangioma associated with thrombo-cytopenia) is a rare disease in infants and ifs hemorrhgic manifestations in these patients are frequently severe enough to threaten life. We experienced a case of this syndrome in a 19 days old boy who had a huge hemangioma on the left upper arm, left anterior chest and back, associated with thrombocytopenia at birth. The patient also had pneumonia of left mid lung and pleural effusion on admission. The hemangioma had progressed rapidly after admission and developed continuous bleeding from the mass in spite of the transfusion of platelet concentrates. He expired on the 3rd hospital day for pneumonia and bleeding. Brief review of the literature was made.
Key Words: Kasabach-Merritt syndrome




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