Three Cases of hereditary Spherocytosis. |
D H Kim, M Y Kim, S Y Kim, J Y Jung |
Department of Pediatrics, Hae Sung Hospital |
한가족에서의 유전성 구상적혈구증 치험 3례 |
김동혁, 김목련, 김수영, 정진영 |
현대 해성병원 소아과 |
Received: 12 July 1987 • Accepted: 2 December 1987 |
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Abstract |
We experienced 3 cases of herediatry spherocytosis which occurred in a family. The family consited
of parents, one sone and one daughter.
The case I, Daughter showed the chief complaints of pallor ad generalized weakness.
The case II, Son hoswed the chief complaint of jaundice.
The case III, Father showed the chief complaints of fatigue and dizziness.
Diagnosis was made by presence of spherocytes in peripheral blood smear, osmotic fragility test,
autohemolysis test, and bone marrow examination.
All 3 patiens were treated by splenectomy, after which symptomatic improvements were very
remarkable.
A brief review of related literature was made. |
Key Words:
Hereditary Spherocytosis |
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