| Hypoplastic Left Heart Syndrome : Report of a Unique Survivor. |
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Hang Bo Cho, Seong Ho Kim, Ha Baik Lee, Kyu Hwang Rhee, Chong Moo Park |
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Department of Pediatrics, College of Medicine, Hanyang University, Seoul, Korea |
| 좌심 저형성 증후군 1례
-장기 생존례- |
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조항보, 김성호, 이하백, 이규환, 박종무 |
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한양대학교 의과대학 소아과학교실 |
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Received: 24 November 1987 • Accepted: 21 January 1988 |
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| Abstract |
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Hypoplastic left heart syndrome is a rare, and fatal congenital heart disease. Most of the patients
with this syndrome die within the 1st month of life. Recently we experienced a hypoplastic left heart
syndrome in a child who was unusually living without surgical intervention for 3 and half years.
The unique clinical course might result from a number of favorable hemodynamic factors and
intact ventricular septum 1) widely patent ductus arteriosus, 2) adequate coronary flow from narrow
ascending aorta, 3) unrestricted pulmonary venous return, and 4) absence of significant vascular
obstructive disease. In addition to the case report, a review of recent literatures was made. |
| Key Words:
Hypoplastic left heart syndrome |
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