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Angioimmunoblastic Lymphadenopathy in a Child.

Journal of the Korean Pediatric Society 1988;31(12):1669-1673.
Published online December 31, 1988.
Angioimmunoblastic Lymphadenopathy in a Child.
S J Lee1, H S Lee1, H S Kim1, C M Kang1, D S Kim2
1Department of Pediatrics, Keimyung Universtiy School of Medicine
2Department of Pathology, Keimyung Universtiy School of Medicine
소아에서 발생한 혈관면역아구성 임파선증 1례
이순정1, 이호석1, 김흥식1, 강진무1, 김동석2
1계명대학교 의과대학 소아과학교실
2계명대학교 의과대학 병리학교실
Received: 20 June 1988   • Accepted: 20 June 1988
Abstract
Angioimmunoblastic lymphadenopathy is a lymphoma like disorder consisting of generalized lymphadenopathy, hepatosplenomegaly, skin rashes, often associated with dysgammag- lobulinemia. We have experienced recently 3 year old female complaining of generalized lymphadenopthy, fever, hepatomegaly and hypergammaglobulinemia, and was proved as angioimmunoblastic lymphadenopathy histologically. Patient was treated with combined chemotherapy with COMP and responded well clinically in 4 months. The brief review of the literature was made.
Key Words: Angioimmunoblastic Lymphadenopathy, Child


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