| A Case of Werdnig-Hoffmann Disease. |
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Ok Ji Hwang, Kon Hee Lee, Ha Joo Choi, Woo Kap Chung |
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Department of Pediatrics, College of Medicine, Hallym University, Seoul, Korea |
| 급성 Werdnig-Hoffmann 병 1례 |
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황옥지, 이건희, 최하주, 정우갑 |
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한림의대부속 강남성심병원 소아과 |
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Received: 8 June 1988 • Accepted: 6 August 1988 |
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| Abstract |
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Acute Werdnig-Hoffmann disease is heredofamilial degeneration of anterior horn cells in the spinal
cord and of motor nuclei in the brain stem, which is clinically characterized by fasciculations of the
tongue, paradoxical respiration, bell shaped thorax, frog-leg posture and intact mentality.
We experienced an 8 month old female infant with acute Werdnig-Hoffmann disease.
We report the case with brief review of some related literatures. |
| Key Words:
Acute Werdnig-Hoffmann Disease |
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