A case of hypertophic cardiomyopathy in newborn infant: An autopsy case. |
Min Shik Kim1, Eun Yong Choi1, Hey Sun Lee1, Young Min Ahn1, Je Geun Chi2 |
1Department, of Pediatrics, Kangnam General Hospital Pub. Corp., Seoul, Korea 2Je Geun Chi, M.D. Department, of Pathology, College of Medicine, Seoul National Univ. Seoul, Korea |
신생아 비대성 심근병증 1례 |
김민식1, 최은영1, 이혜선1, 안영민1, 지제근2 |
1지방공사 강남병원 소아과 2서울대학교 의과대학 병리학교실 |
Received: 20 April 1989 • Accepted: 19 July 1989 |
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Abstract |
Hypertrophic cardiomyopathy is defined as a disorder of heart muscle of unknown cause or
association, and is functionally characterized by a diastolic failure of the left ventricle due to loss of
its normal distensibility.
We subsequently experienced an 18 day old female newborn infant who had suffered from dyspnea,
cyanosis and congestive heart failure since a few days after birth. She died of progressive heart
failure and septicemia by 72 days of age.
Postmortem examination disclosed a typical idiopathic hypertrophic cardiomyopathy showing
prominant interventricular septal hypertrophy, narrow left ventricular cavity and myocardial fiber
disarray. |
Key Words:
Hypertrophic Cardiomyopathy, Newborn, Congestive heart failure |
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