| A case of Dandy-Walker syndrome. |
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Kyung Hee Kim, Jong Leam Choi, Hyo Sook Hong, Wan Seop Kim |
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Department of Pediatrics, Presbyterian Medical Center, Chon Ju, Korea |
| Dandy-Walker 증후군 1례 |
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김경희, 최종림, 홍효숙, 김완섭 |
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전주 예수병원 소아과 |
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Received: 20 April 1989 • Accepted: 7 July 1989 |
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| Abstract |
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Dandy-Walker syndrome is a developmental disorder of the brain associated with hydrocephalus,
possterior fossa cyst and maldevelopment of the cerebellar vermis and is a result of outlet obstruction
of the fourth ventricle.
We experienced a case of a 6 day old male neonate who presented macrocephaly which revealed
marked dilated fourth & lateral ventricle, large posterior fossa cyst and hypoplastic cerebellum, no
vermis on Brain CT. So, he underwent lateral ventriculo-Peritoneal shunt and then his symptoms
progressively improved.
We present a case report with a brief review of the literature. |
| Key Words:
Dandy-Walker syndrome |
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