Journal of the Korean Pediatric Society 1991;34(6):779-786.
Published online June 30, 1991.
The muscular ventricular septal defect and multiple ventricular septal defects in some congenital heart diseases.
Young Hwi Kim1, Ki Soo Kim1, Chung Il Noh1, Jung Yun Choi1, Yong Soo Yoon1, In One Kim2, Kyung Mo Yeon2
1Department of Pediatrics, Seoul National University College of Medicine, Seoul, Korea
2Department of Diagnostic Radiology, Seoul National University College of Medicine, Seoul, Korea
선천성 심질환에서 심실중격 근육부위 결손의 빈도와 다발성 심실중격 결손의 빈도에 대한 연구
김영휘1, 김기수1, 노정일1, 최정연1, 윤용수1, 김인원2, 연경모2
1서울대학교 의과대학 소아과학교실
2서울대학교 의과대학 방사선과학교실
Received: 26 September 1990   • Accepted: 10 December 1990
Abstract
In order to find out the incidences of muscular ventricular septal defect and multiple ventricular septal defects in cases with isolated ventricular septal defect, tetralogy of Fallot, complete endocar- dial cushion defect, complete transposition of the great arteries, corrected transposition of the great arteries and double outlet right ventricle, a retrospective analysis of 620 left ventriculograms were performed. The surgical and echocardiographic findings were also considered to determine the location and number of the defects. The incidences of muscular defect were as follows; ventricular septal defect (2.1%), tetralogy of Fallot (3.1%), complete endocardial cushion defect (0.0%), complete transposition of the great arteries (12.1%), corrected transposition of the great arteries (12.5%) and double outlet right ventricle (9.1%). The incidences of multiple defects were as follows; ventricular septal defect (0.9%), tetralogy of Fallot (3.1%), complete transposition of the great arteries (9.1%), corrected transposition of the great arteries (6.3%) and double outlet right ventricle (9.1%). The incidence of muscular defect in isolated ventricular septal defect was lower than that of western countries. However the incidence of multiple defects in the transposition of the great arteries was not different from the result of the western study. All those who had defect(s) in muscular septum only hade good prognosis. Even in the cases with multiple defects, only a small proportion of the cases had surgically difficult lesions. As the incidence of multiple or muscular defect are very low in isolated ventricular septal defect and echocardigraphic accuracy of identifying muscular defect approaches 85%, the oriental patients with isolated ventricular septal defect may undergo surgical correction without invasive studies with neglible risk of residual muscular defect.
Key Words: multiple ventricular septal defect, Muscular ventricular septal defect




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