Tricuspid atresia associated with double orifice mitral valve and coronary sinus septal defect. |
In Sook Park1, Ki Soo Kim1, Young Seo Park1, Chang Yee Hong1, Shi Joon Yoo2, Meong Gun Song3 |
1Department of Pediatrics, Asan Medical Center, Ulsan University, Seoul, Korea 2Department of Radiology, Asan Medical Center, Ulsan University, Seoul, Korea 3Department of Thoraic Surgery, Asan Medical Center, Ulsan University, Seoul, Korea |
양판구성 승모판과 관정맥동 중격결손을 동반한 삼첨판 폐쇄 1례
- 칼날 및 풍선 심방중격 절개술과 양방향 공정맥 폐동맥 단락으로 치료한 예 - |
박인숙1, 김기수1, 박영서1, 홍창의1, 유시준2, 송명근3 |
1울산대학교 의과대학 소아과학교실 2울산대학교 의과대학 방사선과학교실 3울산대학교 의과대학 흉부외과학교실 |
Received: 28 December 1990 • Accepted: 13 March 1991 |
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Abstract |
Clinical, echocardiographic and angiographic findings of a very rare case of cardiac malformation
is presented. The main features were tricuspid atresia, coronary sinus septal defect, and double orifice
mitral valve. These defects were correctly diagnosed by echocardiography and were confirmed by
angiocardiography. This patient was palliated successfully with blade balloon atrial septostomy and
bidirectional cavopulmonary shunt.
To the best of our knowledge, this is the first reported case of such a combinatin of congenital
cardiac malformations in English literature. Also we believe this is the first report of blade atrial
septostomy performed in Korea. |
Key Words:
Tricuspid atresia, Double orifice mitral valve, Coronary sinus septal defect, Blade atrial septostomy, Bidirectional cavo-pulmonary shunt |
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