Korean Journal of Pediatrics 2009;52(12):1388-1391.
Published online December 15, 2009.
The first Korean case of poland-Möbius syndrome associated with dextrocardia
Jiyoung Jung, Han Gyu Kim, Hae-Mi Ahn, Su Jin Cho, Eun Ae Park
Department of Pediatrics, School of Medicine, Ewha Womans University, Seoul, Korea
Poland-Möbius syndrome 신생아 1례
정지영, 김한규, 안혜미, 조수진, 박은애
이화여자대학교 의학전문대학원 소아과학교실
Correspondence: 
Eun Ae Park, Email: pea8639@ewha.ac.kr
Abstract
Poland syndrome is characterized by unilateral absence or hypoplasia of the pectoralis muscle and variable degree of ipsilateral hand anomalies. Möbius syndrome is a congenital neurological disorder characterized by complete or partial facial paralysis. Although the pathogeneses of these diseases are not well-characterized, diminished blood flow to the affected side is thought to play a role. A male infant weighing 2.670 g was born at 38+3 weeks of gestation with left facial paralysis, left chest wall defect with dextrocardia, and symbrachydactyly between the second and third fingers. The combination of Poland–Möbius syndrome is rare, and only 2 cases associated with dextrocardia have been reported worldwide. Here, we report the first case of Poland-Möbius syndrome associated with dextrocardia in Korea.
Key Words: Poland-Mö, bius syndrome, Dextrocardia


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