Korean Journal of Pediatrics 2008;51(1):98-101.
Published online January 15, 2008.
Primary leiomyosarcoma of the chest wall in a child : a case report
Jae Hyuk Choi, David Chanwook Chung, Mee Jeong Lee
Department of Pediatrics, Dankook University College of Medicine, Cheonan, Chungnam, Korea
소아의 흉벽에서 진단된 평활근육종 1례
최재혁, 정찬욱, 이미정
단국대학교 의과대학 소아청소년과학교실
Correspondence: 
Mee Jeong Lee, Email: LMJPED@dankook.ac.kr
Abstract
Leiomyosarcoma is an uncommon soft tissue sarcoma of mesenchymal cell origin, which shows smooth muscle differentiation. Leiomyosarcoma is seldom found in the pediatric population, and accounts for fewer than 2% of all soft tissue sarcomas. Leiomyosarcoma of the chest wall is extremely rare in children. We report here a case of an 8-year-old boy with a primary leiomyosarcoma that was incidentally found as a rib mass. The patient underwent a complete resection for a suspected osteochondroma diagnosed by a three-dimensional chest computed tomography examination. Pathological findings of the mass revealed intersecting fascicles of spindle cells showing cigar-shaped nuclei, inconspicuous nuclear pleomorphism and occasional mitotic figures in the background of a suspected osteochondroma of the rib. This report documents the first description of a leiomyosarcoma possibly arising in an osteochondroma of the rib in a child.
Key Words: Leiomyosarcoma, Chest wall, Rib, Osteochondroma, Child


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