| Small Intestinal Infarction Associated with Henoch-Schöenlein Purpura |
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Myung Ki Han1, Yu In Park1, Jeong Ho Kim1, Jung Joo Lee1, Hye Young Kang2 |
1Department of Pediatrics, Kangnung Hospital, College of Medicine, Ulsan University, Kangnung, Korea
1Department of Pediatrics, Kangnung Hospital, College of Medicine, Ulsan University, Kangnung, Korea
2Yonsei Pediatric Clinic, Korea |
| Henoch-Schöenlein 자반증에 병발한 장경색 1례 |
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한명기1, 박유인1, 김정호1, 이정주1, 강혜영2 |
1울산대학교 의과대학 강릉병원 소아과
1울산대학교 의과대학 강릉병원 소아과
2연세소아과 |
Correspondence:
Yu In Park, Email: yipark@knh.co.kr
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| Abstract |
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Henoch-Schöenlein purpura, also known as anaphylactoid purpura, is characterized by palpable
purpura, colicky abdominal pain, gastrointestinal hemorrhage, arthralgias, and renal involvement.
Histopathologically, the condition represents a vasculitis, and in fact, it may be the most common
vasculitis syndrome affecting children. The pathogenesis of Henoch-Schöenlein purpura remains
poorly understood, but it is postulated that an unknown antigenic stimulus causes elevation of
circulating IgA and that complement activation leads to necrotizing vasculitis. All of its clinical
features are attributable to wide spread vasculits. Abdominal pain is the most common gastrointestinal
symptom, but intestinal bleeding and intussusception may occur. Mesenteric vasculitis is a
rare but potentially serious complication of systemic vasculitis. It is reported in association with
rheumatoid arthritis, systemic lupus erythematosus, scleroderma, polyarteritis nodosa, and giant
cell arteritis in adult patients. Typical features are diffuse non-specific abdominal pain progressing
on occasion to gastrointestinal hemorrhage, perforation, or more rarely infarction. Fortunately intestinal
infarction is a rare complications, but if present carries a high chance of mortality, and
swift management of the underlying vasculitis is crucial. We describe here an unusual case of a
small intestinal infarction associated with Henoch-Schöenlein purpura caused by mesenteric vasculitis. |
| Key Words:
Henoch-Schö, enlein purpura, intestinal infarction |
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