| A Case of Isolated Right Ventricular Hypoplasia without Tricuspid Atresia or Pulmonary Atresia |
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Eui Jun Yang1, Sun Young Kim1, Sank Ook Nam1, Hee Ju Park1, Nam Hee Kwak2 |
1Department of Pediatrics, College of Medicine, Pusan National University, Pusan, Korea
2Department of Pediatrics, Munwha Hospital, Pusan, Korea |
| 삼첨판 폐쇄와 폐동맥 폐쇄를 동반하지 않은 우심실 형성 부전증 1례 |
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양의준1, 김선영1, 남상욱1, 박희주1, 곽남희2 |
1부산대학교 의과대학 소아과학교실
2문화병원 소아과 |
Correspondence:
Eui Jun Yang, Email: 1
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| Abstract |
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Isolated right ventricular hypoplasia, unassociated with severe pulmonary or tricuspid valvar malformations, is a rare primary congenital cardiac anomaly in which of the trabecular portion of right ventricle fails to develop. An atrial septal defect or a patent foramen ovale serves as an escape valve. We observed a 2-day-old neonate with this disorder who suffered from cyanosis. The diagnosis was made by Doppler-echocardiography which revealed marked reduction in right ventricular size and right-to-left shunt through the atrial septal defect. There was no other cardiac malformation such as pulmonary atresia or tricuspid atresia. |
| Key Words:
Isolated right ventricular hypoplasia, Congenital heart disease |
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