Journal of the Korean Pediatric Society 1999;42(7):1026-1030.
Published online July 15, 1999.
A Case of Isolated Right Ventricular Hypoplasia without Tricuspid Atresia or Pulmonary Atresia
Eui Jun Yang1, Sun Young Kim1, Sank Ook Nam1, Hee Ju Park1, Nam Hee Kwak2
1Department of Pediatrics, College of Medicine, Pusan National University, Pusan, Korea
2Department of Pediatrics, Munwha Hospital, Pusan, Korea
삼첨판 폐쇄와 폐동맥 폐쇄를 동반하지 않은 우심실 형성 부전증 1례
양의준1, 김선영1, 남상욱1, 박희주1, 곽남희2
1부산대학교 의과대학 소아과학교실
2문화병원 소아과
Correspondence: 
Eui Jun Yang, Email: 1
Abstract
Isolated right ventricular hypoplasia, unassociated with severe pulmonary or tricuspid valvar malformations, is a rare primary congenital cardiac anomaly in which of the trabecular portion of right ventricle fails to develop. An atrial septal defect or a patent foramen ovale serves as an escape valve. We observed a 2-day-old neonate with this disorder who suffered from cyanosis. The diagnosis was made by Doppler-echocardiography which revealed marked reduction in right ventricular size and right-to-left shunt through the atrial septal defect. There was no other cardiac malformation such as pulmonary atresia or tricuspid atresia.
Key Words: Isolated right ventricular hypoplasia, Congenital heart disease


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