Two Cases of Total Colon Aganglionosis Involving Small Bowel in Triplet |
Won A Park, Hyun Joo Kim, Kyung Dug Moon, Hea Kyoung Lee, Young Hee Yu, Hyun Suk Lee |
Department of Pediatrics,Korea Veterans Hospital, Seoul ,Korea |
삼태아에서 발생한 소장까지 침범한 전대장 무신경절증 2례 |
박원아, 김현주, 문경덕, 이혜경, 유영희, 이현숙 |
한국보훈병원 소아과 |
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Abstract |
Total or mostly total intestinal aganglionosis is rare and invariably fatal.
All patients with aganglionosis involving more than half of the small bowel have died with persistent intestinal obstruction and secondary maluntrition and infection.
Recently, we experienced two cases of total colon aganglionosis extending to the middle of the jejunum in triplet.
We report the cases with brief review of literatures. |
Key Words:
Total colon aganglionosis, Small bowel |
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