| A Case of Phakomatosis Pigmentovascularis |
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Seung Mo Park1, Kook In Park1, Hye Jung Joo1, Ran Namgung1, Chul Lee1, Dong Gwan Han1, Soo Il Chun2 |
1Department of Pediatrics, Yonsei University, College of Medicine, Seoul, Korea
2Department of Dermatology, Yonsei University, College of Medicine, Seoul, Korea |
| 색소혈관 모반증 1례 |
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박승모1, 박국인1, 주혜정1, 남궁란1, 이철1, 한동관1, 전일수2 |
1연세대학교 의과대학 소아과학교실
2연세대학교 의과대학 피부과학교실 |
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| Abstract |
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In 1947, Ota et al. First reported a case of phakomatosis pigmentovascularis and defined a subgroup of this disease having a congenital generalized hemangioma and pigmented lesions including anmongolian spot-like lesion, nevus pigmentosus and nevus of Ota.
We experienced a case of phakomatosis pigmentovascularis type Iib in a 10-day old male baby, who since birth, had generalized nevus flammeus and blue spots, syndactyle between 2nd and 3rd toes in both feet, and dilated collecting system in left kidney. |
| Key Words:
Phakomatosis pigmentovascularis, Nevus flammeus, Blue spot, Syndactyly, Dilated collecting system |
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