All issues > Volume 32(11); 1989

Original Article

J Korean Pediatr Soc. 1989;32(11):1560-1567. Published online November 30, 1989.

A case of hypertophic cardiomyopathy in newborn infant: An autopsy case.

Min Shik Kim¹, Eun Yong Choi¹, Hey Sun Lee¹, Young Min Ahn¹, Je Geun Chi²

¹Department, of Pediatrics, Kangnam General Hospital Pub. Corp., Seoul, Korea
²Je Geun Chi, M.D. Department, of Pathology, College of Medicine, Seoul National Univ. Seoul, Korea

Received: April 20, 1989;  Accepted: July 19, 1989.

Abstract

Hypertrophic cardiomyopathy is defined as a disorder of heart muscle of unknown cause or association, and is functionally characterized by a diastolic failure of the left ventricle due to loss of its normal distensibility. We subsequently experienced an 18 day old female newborn infant who had suffered from dyspnea, cyanosis and congestive heart failure since a few days after birth. She died of progressive heart failure and septicemia by 72 days of age. Postmortem examination disclosed a typical idiopathic hypertrophic cardiomyopathy showing prominant interventricular septal hypertrophy, narrow left ventricular cavity and myocardial fiber disarray.

Keywords :Hypertrophic Cardiomyopathy, Newborn, Congestive heart failure