All issues > Volume 32(11); 1989

Original Article

J Korean Pediatr Soc. 1989;32(11):1586-1591. Published online November 30, 1989.

A case of Dandy-Walker syndrome.

Kyung Hee Kim¹, Jong Leam Choi¹, Hyo Sook Hong¹, Wan Seop Kim¹

¹Department of Pediatrics, Presbyterian Medical Center, Chon Ju, Korea

Received: April 20, 1989;  Accepted: July 7, 1989.

Abstract

Dandy-Walker syndrome is a developmental disorder of the brain associated with hydrocephalus, possterior fossa cyst and maldevelopment of the cerebellar vermis and is a result of outlet obstruction of the fourth ventricle. We experienced a case of a 6 day old male neonate who presented macrocephaly which revealed marked dilated fourth & lateral ventricle, large posterior fossa cyst and hypoplastic cerebellum, no vermis on Brain CT. So, he underwent lateral ventriculo-Peritoneal shunt and then his symptoms progressively improved. We present a case report with a brief review of the literature.

Keywords :Dandy-Walker syndrome