Journal of the Korean Pediatric Society 1986;29(10):1152-1156.
Published online October 31, 1986.
A Case of Potter Syndrome Type I.
Jong Cheol Ryu1, Jae Kwang Hong1, Jun Taek Park1, Jung Sik Min1, Chang Jee Choi1, Je Geun Chi2
1Department of Pediatrics, Seoul Adventist Hospital
2Department of Pathology, Seoul National University
Potter Syndrome (type I) 1 례
류종철1, 홍재광1, 박준택1, 민정식1, 최창희1, 지제근2
1서울위생병원 소아과
2서울대학교 의과대학 병리학교실
Abstract
We have experienced a case of Potter syndrome type I in a newborn infant who presented with severe respiratory distress soon after birth. The diagnosis was made with autopsy findings consisted of bilateral polycystic renal dysplasia, bilateral hypoplastic lung , facies renalis, fibrocystic change of liver, patent ductus arteriosus, patent foramen ovale, ureter and urinary bladder hypoplasia and calcaneovarus. Brief reviews of the related literatures are given.
Key Words: Potter syndrome type I, Facies renalis, Hypoplastic lung, Polycystic renal dysplasia.




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