| Cardiac Tumor in Children. |
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Eun Jung Bae, Young Hwue Kim, Jung Yun Choi, Yong Seung Hwang, Hyo Seop Ahn, Yong Soo Yun |
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Department of Pediatrics, Seoul National University College of Medicine, Seoul, Korea |
| 소아기의 심장종양에 대한 임상적 고찰 |
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배은정, 김영휘, 최정연, 황용승, 안효섭, 윤용수 |
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서울대학교 의과대학 소아과학교실 |
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Received: 28 April 1990 • Accepted: 21 August 1990 |
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| Abstract |
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Primary cardiac tumor is very rare and has been a medical curiosity but is potentially curable by
current management with improvements of the imaging apparatus and the surgical technique.
Metastatic cardiac tumor is also very rare and is more difficult to diagnose than primary ones
because of lack of specific symptoms.
Twelve cases of cardiac tumor, collected from 1978 to 1989 at the Department of Pediatrics, Seoul
National University Hospital were investigated in order to analyse clinical features and laboratory
findings especially echocardiographic results.
In the period of 11 years, there were 10 cases of primary cardiac tumors (7 cases of rhabdomyoma,
1 case of fibroma, 1 case of myxoma and 1 case of uncertain type) and 2 cases of metastatic tumors.
All the cases of rhabdomyoma were associated with tuberous sclerosis and 4 out of 7 cases were
presented with seizure in infancy. Among 12 cases, cardiac murmur was detected in 4 (33%) and
tachyarrhythmia in 1 (8%) and heart failure in 4 (33%). No significant cardiac symptoms or signs were
found in 5 from 12 cases. Chest X-ray showed cardiomegaly and/or abnormal cardiac contour in
about half of the cases and the rest half showed no abnormalities. Two-dimensional echocardiogram
was performed in 8/10 primary cardiac tumor and 2/2 metastatic tumor. It showed multiple masses
involving ventricles and ventricular septum in rhabdomyoma. In two cases of metastatic tumor,
echocardiogram showed not only intracardiac tumor masses, but also the original masses around the
heart and attached vessels.
Cardiac rhabdomyoma is not rare and often found in tuberous sclerosis patients even in the cases
without any cardiac symptoms or signs. Two-dimensional echocardiogram seems useful not only in
making diagnosis but also in assessing tumor extent and its hemodynamic impact. |
| Key Words:
Cardiac tumor, Rhabdomyoma, Tuberous sclerosis, Metastatic tumor |
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