Journal of the Korean Pediatric Society 1991;34(6):869-876.
Published online June 30, 1991.
A case of myelofibrosis with juvenile xanthogranuloma.
Jong Chan Kim1, Hae Yong Lee1, Hwang Min Kim1, Baek Keun Lim1, Jong Soo Kim1, Young Hyuk Lee2
1Department of Pediatrics, Yonsei University, Wonju College of Medicine, Wonju, Korea.
2Department of Pediatrics, Min Joong HospitaI,Konkuk University, College of Medicine
연소성 황색육아종과 동반된 골수섬유증 1례
김종찬1, 이해용1, 김황민1, 임백근1, 김종수1, 이영혁2
1연세대학교 원주의대 소아과학교실
2건국대학교부속 민중병원 소아과
Received: 20 November 1990   • Accepted: 26 February 1991
Abstract
Myelofibrrosis is characterized by anemia, leukoerythroblastosis, extramedullary hematopoiesis, hepatosplenomegaly, osteosclerosis and fibrosis of bone marrow. Idiopathc myelofibrosis is usually a disease of the adult and is rare in the pediatric age group. Juvenile xanthogranuloma is characterized by multiple papules on forehead and scalp. Lipid laden histiocytes and Touton giant cell are found in skin biopsy. We experienced a case of myelofibrosis with juvenile xanthogranuloma. So, we presented the case and brief review of literatures.
Key Words: Mylofibrosis, Juvenile xanthogranuloma




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