An Autopsy Case of Double Aortic Arch |
Ji Sook Kim1, Yong Myung Jo1, Kyung Hee Ko1, Eun Ryoung Kim1, Je Grun Chi2 |
1Department of Pediatrics, Sung-Ae General Hospital, Seoul, Korea 2Department of Pathology, Seoul National University College of Medicine, Seoul, Korea |
중복 대동맥궁 부검 1례 |
김지숙1, 조용명1, 고경희1, 김은령1, 지제근2 |
1성애병원 소아과 2서울대학교 의과대학 병리학교실 |
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Abstract |
Double aortic arch is the most common type of symptomatic vascularring. In most
patients, the symptoms are manifested at birth or in early infancy. Double aortic arch usually has more severe symptoms than other types of complete vascular rings.
We experienced one case of complete duplicated double aortic arch with left
descending aorta and left patent ductus arteriosus. A one-day-old female neonate was
transferred to our hospital because of mild dyspnea and stridor. She showed intractable CO2 retention and respiratory difficulty with time in spite of ventilator therapy. She died of respiratory failure 23 hours after birth. On autopsy, we found that the diameter of the vascular ring was 0.7cm in maximum extent. It was ovoid and contained trachea and esophagus. The trachea was flattened due to allowing 0.1¡¿0.2cm. The compression level of the trachea was approximately 1cm from the tracheal bifurcation. |
Key Words:
Double aortic arch, Congenital heart disease, Respiratory distress |
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