Authors experienced a case of Morquio’s syndrome accompanied by respiratory failure in a aged fifteen year old boy. Patient showed normal intelligence, but stunted growth with short trunk and unproportionately large head, pectus carinatum, kyposcoliosis, muscular weakness, paralysis and genu valgum. No other member of family was affected with this syndrome. There were radiological findings of subluxation between first and second cervical vertevrae, central beaking with... |
In the newborn, a complete occlusion of the pyloric outlet is an extremely rare event. Authors experienced a case of pyloric atresia in a 2-day old boy, Who was admitted because of nonbilious vomiting. The plain radiograph of the abdomen showed gas in the huge stomach, but no gas noted distally. At operation, 3 days after birth, the pylorus was atretic... |
The β-thalassemia minor is a hereditary microcytic, hypochromic anemia characterized by decerased producion of β-globin polypeptide chain. The β-thalassemia minor should be clinically differentiated from iron deficiency anemia. The thalassemia are common in the Medeterranean region, the Middle Ease, the Africa, Indea, and Thailand, but rare in Korea. The authors experienced two cases of familial β-thalassemia minor 4-year 7-month-old female patient and... |
The auther analysed 29 patients who were treated with prednisolone, including nephrotic syndrome(13 cases). Acute leukemia (10 cases), bronchial asthma(2 cases), juvenile rheumatoid arthritis(2 cases) and ulcerative colitis(1 cases) patients in childhood, after remission induction, prolonged alternate or interrupted treatment was used. The auther observed patterns of height velocity of these patients from 1.6 to 10.3 years. The results were as... |
To evaluate the atlantoaxial instability in children with Down syndrome, the authors analyzed the 97 children with Down syndrome attending to 2 schools for handicaped children in Pusan. The results of study were as follows; 1) The incidence of atlantoaxial instability in 97 individuals with Down syndrome was 8(8.3%) in neutral position and in 10(10.3%) in flexion, respectively. 2) The mean atlantoaxial gap... |
The autor analysed foreign body in the airway, divided into two groups vegetable foreign body group(VFBG) and non-vegetable foreign body group(N-VFBG), according to the nature, in 88 patients aged from 5 months to 15years who were diagnosed and treated under ventilating bronchos copy at Department of Pediatrics and Otolaryngology, Pusan National University Hospital from 1980 to 1990. Of the 88... |
A female infant at 38 days of age was admitted to pediatric department of Pusan National University hospital due to dehydration, weight loss, vomiting, polyuria. Physical exmination at the time of admission revealed a slightly anemic, moderately dehydrated, dwarfed female infant in no acute distress. Laboratory studies on admission revealed hypokalemic, hyperchloremic metablic acidosis with normal anion gap and persistent... |
The clinical picture of beingn recurrent intrahepatic cholestasis (BRIC) consists of multiple epi- sodes of cholestatic jaundice without extrahepatic bile duct obstruction. Since first description by Summerskill and Walshe in 1959, almost 100 patients with BRIC have been described. The mechanism involved in the initiation and perpetution of an episode of cholestasis are unknown. Altered bile acid metabolism has been proposed to play a... |
In this study, we evaluated clinical symptoms, neurologic findings, CSF examinations and prognosis of patients who were diagnosed to have tuberculous meningitis at Pusan National University Hospital and Gospel Hospital from march, 1983 to december, 1989. 1) Mean age was 3 years and 8 months and the percentage of patients under 6 years old was 71.9%. The male to female ration was 2.2:1. 2) Fever and vomiting... |
The authors analyzed the clinical features, and the therapeutic responses in 29 patients with juvenile rheumatoid arthritis who were diagnosed and followed at Department of Pediatrics, Pusan National University Hospital from 1980. 1 to 1990. 6. The following results were obtained 1) Of the total 29 patients, 12cases (41.4%) were pauciarticular type II and 7cases (24.2%) were polyarticular RF(—) type. Seventeen cases (58.7%) were 8-11 yrs... |
Twenty one cases of childhood fulminant hepatitis admitted to Pediatric department of Pusan National University Hospital form Jan. 1979 to Sep. 1989 were analysed. The results were as follows; 1) Age distribution was from 8 months to 13 yerars old and 66.7% of the patients were 2 to 9 year old of age. In sex ratio, male to female was 1,6:1. 2) Presumable etiologic factors were HBV... |
To evaluate the growth status of Congenital Heart Disease, we analyzed the 69 children with Ventricular Septal Defect who were admitted to Pediatric department and Chest Surgery department, Pusan National University Hospital from January, 1986 to June, 1987. The result of study were as follows: 1) This group was composed of 69 consecutive operation on children with ventricular septal defect. The sex distribution chanced to be... |
The authors have analysed the clinical characteristics of 117 cases of teenage pregnancy and their 122 newborn cases who were visited Pusan National University Hospital and Hae Sung Hospital from January 1982 to August 1988. The results were summarized as follows; 1) The youngest teenage mother was 14 years old, and below 17 years old was 28.2% and the remainder were between 18 and 19 years... |
Clinical, bacteriologic and radiologic studies were performed in 63 infants and children with urinary tract infection who were admitted to Department of Padiatrics, Pusan National University Hospital from March 1982 to February 1988. The results were summarized as follows: 1) UTI was more prevalent in infancy and early childhood (71.4%). Sex distribution was similar in all age group, and male was more prevalent in infancy and... |
To elucidate the characteristics of immunoregulatory system of children with chronic active hepatitis B and hepatitis B vaccine inoculated infant, the authors examined T cell subsets of the peripheral blood in 16 children with asymptomatic HBsAg carriers, 19 children with chronic hepatitis B (11 chronic persistent hepatitis (CPH) and 8 chronic active hepatitis (CAH) and 21 hepatitis B vaccine inoculated infants as well as... |
Desquamative interstitial pneumonia (DIP) is a variant of idiopathic interstitial pneumonias, but characteristicalIy has massive desquamation and proliferation of alveolar cells into the distal air space with minimal fibrosis of the alveolar wall. DIP seems to have better response to corticosteroid and benign prognosis than idiopathic interstitial pneumonia. We experienced one case of 6-year old girl who showed typical picture of DIF on lung... |
A 9-year-old girl with Addison’s disease without other endocrine disorder presented with a brief review of the literature. The patient was transferee! to our hospital because of darkish brown pigmentation of whole body and generalized weakness which had misunderstood cyanotic heart disease. On physical examination, she was poorly nourished and below 10 percentile in weight and height. Skin and mucous membrane were diffusely darkish brown,... |
The author has analysed 1080 cases of Pediatric patients visited Pediatric or psychiatric depart- ment for behavioral, emotional, or Psychiatric problems, from July 1982 to June 1987. The patients were categorized into three groups to observe the distribution of age, sex and disease, and the relation of symptom and disease, 127 cases consulted to Psychiatric department, 356 cases visited Psychiatric department directly, and 597... |
To evaluate the influence of nephrotic syndrome on the thyroid function test in children, serum T3, T4, free T4, TSH, TBG and rT3 were measured using radioimmunoassay in 14 clinically euthyroid children with nephrotic syndrome who were admitted to Department of Pediatrics, Pusan National University Hospital from July, 1986 to August, 1987. Control group was 15 children who visit our outpatient department for minor... |
We experienced two cases of Klippel-Trenaunay-Weber Syndrome in 13 years old boy and 10 years old girl. They had shown large nevus flammeus, varicose veins, soft tissue and bong hypatrophy. In angrogam and venogram capillary and venous hemangioma were noted, but we could not find arteriovenous filstula. We report two cases of Klippel-Trenaunay-Weber Syndrome with review of literature. |
Clinical study was carried out on 149 congestive heart failure(CHF) cases of 873 heart disease patients admitted to the Department of Pediatics, Pusan National University Hospital from January 1980 to June 1987 and performed various diagnostic evaluations, especially liver function tests. The results obtained were as follows. 1) The congenital (CHD) and acquired (AHD) cause of heart disease were each 75.9% and 19.0% and the rest,... |
Congenital absence of spleen is often associated with malpositions and malformations of other organ system such as congenital heart disease partial situs inversus, symmetric lobulation of the liver and the lungs. This is a rare syndrome but has been reported in increasing frequency in recent years. The pure congenital asplenia is a very rare disease. We experienced two cases of congenital asplenia. One is... |
Department of Pediatrics, College of Medicine, Pusan National University Wilson’s disease is due to excessive accumulation of copper in the liver, brain, kidneys and cornea caused by a defect in biliary excretion. The classic presentation of Wilson’s disease is the triad of neurologic abnormalities, Kayser- Fleischer ring and cirrhosis associated with low serum copper and ceruloplasmin levels. The case, 12-year-old boy, suffered from jaundice, abdominal... |
Relapsing polychondritis is a rare disease characterized by recurring episodes of inflammation of the cartilagenous structures of the body. Commonly involved organs include the inner and external ear, nose, joints, eyes, tracheobronchial tree, and cardiovascular system. We experienced a case of relapsing polychondritis in a 4 year old boy with auricular chondritis, polyarthritis, nasal chondritis, laryngeal chondritis and episcleritis. The review of... |
A clinical study was performed on 7,534 cases of disease entity and course in adolescence who were admitted to various department including internal medicine, pediatrics in Pusan National University Hospital from January 1980 to December 1985.The results are as follows: 1) The age distribution was from 10 years to 20 years of age which was devided to early adolescence in 21.2%,... |
Takayasu’s arteritis is an arteritis of undetermined etiology which affects the aorta, the proximal portions of its major branches and pulmonary arteries. This 6 4/12-year-old female patient was developed hypertension and convulsion during" admission. At first we suspect rheumatic heart disease because of carditis, arthralgia, elevation of ESR, and presence of CRP and ASLO. But hypertension and congestive heart... |
This is a case of cryptococcosis accompanied by pulmonary tuberculosis and malnutrition. The 11-year-old female patient was admitted to our hospital because of dyspnea, ascites and oliguria. Cervical lymph node biopsy and chest X-ray were checked, which were revealed tuberculous lesions. She was treated with amphotericin-B for 10 weeks, but didn*t complete remission at present. |
The author experienced a case of spondylothoracic dysplasia from 4 month old female-patient who had congenital anomalies on vertebrae & thorax. She was born with normal weight and full term, but she looked bizarre because of shortened trunk & neck, marked protuberant abdomen, prominent lumbar lordosis. On admission, she had growth retardation for having upper respiratory tract infection and feeding... |
For evaluation of clinical characteristics, 228 cases of neck mass in childhood were reviewed, which were surgically removed and pathologically diagnosed during the period from January 1973 to August 1984 at the pediatric department of Pusan National University Hospital. The results are summarized as follows: 1)Histologically the most common lesion was nonspecific lymphadenitis (31.6%) and next was tuberculous lymphadenitis(17.1%). The congenital... |
The author observed serum alpha-fetoprotein concentration in 112 cases of healthy, fullterm newborns and infants from March 1984 to September 1984. Among them, 9 cases were cord bloods of healthy, full-term newborns who were delivered at Pusan St. Benedict Hospital, the others were healthy infants under the age of 36 months who visited well-baby-clinic of Pusan St. Benedict Hospital. The... |