| A Case of Moyamoya Disease with Focal Seizure. |
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Man Gee Hong, Hak Ki Kim, Kyung Tai Whang, Sung Hoon Cho |
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Department of Pediatrics, Catholic Medical College, Seoul, Korea |
| 촛점성 경련을 보인 Moyamoya 병 의 수술치험 1 례 |
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홍만기, 김학기, 황경태, 조성훈 |
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가롤릭의과대학 소아과학교실 |
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| Abstract |
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We experienced a case of Moyamoya syndrome in a 4 year-old girl. The patient was well
until 3 years of age when she first experienced numbness of the left arm. After 10 days of
above episode, she had tonic-clonic movements of left sided extremities which lasted,
approximately 2 hours and followed by paresis.
During the following week the second attack of focal seizure followed by paresis of left
arm occurred, and the patient was admitted for evaluation, and work-up of seizure disorder.
Metabolic work-up consisted of calcium, phosphorus, electrolytes and blood sugar, and all
of which were normal. EEG showed diffuse slowing into delta range activity and frequent
sharp bursts in the right temporal head areas with phase reversal at T< area.
Brain CT scan revealed mixed vat density in the right frontoparietal region (Fig. 1). To
clarify the matter, right carotid angiography was performed and showed narrowing of
internal carotid artery and its major branches, occlusion of middle cerebral artery, and
abnormal capillary net-works (Fig. 2).
Above findings were felt that the focal seizure was secondary to Moyamoya syndrome.
On. 11th hospital days, she underwent operation named encephaloduroarteriosynangiosis.
The patient was discharged in satisfactory condition at 24th hospital days, and has been
seizure free over 8 months on phenobarbital 30mg twice daily.
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| Key Words:
Moyamoya Disease, Focal Seizure, Carotid Angiography, Encephaloduroarteriosynangiosis. |
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