A case of congenital dyserythropoietic Anemia.

Na, Sang Oh; Ha, Seong Hoon; Koo, Hong Hoe; Shin, Hee Young; Ha, Il Soo; Ahn, Hyo Seop; Oh, Doek Ja; Park, Myoung Hee

Original Article

Journal of the Korean Pediatric Society 1990;33(3):410-415.
Published online March 31, 1990.

A case of congenital dyserythropoietic Anemia.

Sang Oh Na¹, Seong Hoon Ha¹, Hong Hoe Koo¹, Hee Young Shin¹, Il Soo Ha¹, Hyo Seop Ahn¹, Doek Ja Oh², Myoung Hee Park²

¹Department of Pediatrics, College of Medicine, Seoul National University, Seoul, Korea
²Department of Clinical Pathology, College of Medicine, Seoul National University, Seoul, Korea

Congenital Dyserythropoietic Anemia 1례

나상오^¹^, 하성훈^¹^, 구홍회^¹^, 신희영^¹^, 하일수^¹^, 안효섭^¹^, 오덕자^²^, 박명희^²

^¹서울대학교 의과대학 소아과학교실
^²서울대학교 의과대학 임상병리학교실

Received: 29 September 1989 • Accepted: 29 September 1989

Abstract

The congenital dyserythropoietic anemia refers to a group of hereditary disorders of erythropoiesis characterized by ineffective erythropoiesis, multinuclearity of erythroblasts, and secondary hemo- chromatosis. The authors report a case of anemia in a 4 month-old girl whose bone marrow showed dyserythropoietic features. A brief review of referential literatures was made.

Key Words: Dyserythropoietic anemia, Congenital