Hemophagocytic Syndrome with Kawasaki
Disease and Peripheral Gangrene |
Hwa Jun Yun1, Ko Woon Jeon1, Hwang Min Kim1, Seok Won Park1, Young Uh2 |
1Department of Pediatrics, Yonsei University, Wonju College of Medicine, Wonju, Korea 2Department of Clinical Pathology, Yonsei University, Wonju College of Medicine, Wonju, Korea |
가와사끼병 및 말단 조직 괴저가 동반된혈구탐식 증후군 1례 |
윤화준1, 전고은1, 김황민1, 박석원1, 어영2 |
1연세대학교 원주의과대학 소아과학교실 2연세대학교 원주의과대학 임상병리학교실 |
Correspondence:
Hwang Min Kim, Email: khm9120@wonju.yonsei.ac.kr |
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Abstract |
A twenty six months-old boy developed hemophagocytic syndrome during the course of Kawasaki disease. Despite the appropriate treatment modalities for Kawasaki disease, he developed thrombocytopenia, hepatomegaly, high-grade fever, hypertriglyceridemia, peripheral gangrene, and evidence of hemophagocytosis in bone marrow biopsy. Although the course was stormy, he responded well to a combination therapy of corticosteroid and etoposide. |
Key Words:
Etoposide, Hemophagocytic syndrome, Bone marrow biopsy, Kawasaki disease, Peripheral gangrene |
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