| Study of Congenital Mitral Stenosis Cases Requiring Surgical Correction in the First 2-Years of Life |
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In Seung Park1, Young Seok Lee1, Mi Young Han1, Jae Young Lee1, Soo Jin Kim1, Do Jun Cho1, Mee-Hye Oh2, Woong-Han Kim3, Young-Tak Lee3, Eun Jung Bae4, Seong Ho Kim5 |
1Department of Pediatrics, Sejong General Hospital, Pucheon, Korea
2Department of Pathology, Sejong General Hospital, Pucheon, Korea
3Department of Surgery, Sejong General Hospital, Pucheon, Korea
3Department of Surgery, Sejong General Hospital, Pucheon, Korea
4Department of Pediatrics, Seoul National University, College of Medicine, Seoul, Korea
5Department of Pediatrics, Gachon Medical University, Incheon, Korea |
| 2세 미만에서 수술적 교정이 필요했던 선천성 승모판협착에 대한 연구 |
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박인승1, 이영석1, 한미영1, 이재영1, 김수진1, 조도준1, 오미혜2, 김웅한3, 이영탁3, 배은정4, 김성호5 |
1세종병원 소아과
2세종병원 해부병리과
3세종병원 흉부외과
3세종병원 흉부외과
4서울대학교 의과대학 소아과학교실
5가천의과대학교 소아과학교실 |
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| Abstract |
Purpose
: Congenital mitral stenosis(CMS) is a rare anomaly accounting for 0.4-0.5% of total heart disease. CMS which cases needed surgical correction in infancy are even rare. In this study, we analyzed 11 CMS patients of less than 2 year of age who needed surgical corrections, in order to find out their diagnoses, the characteristics, the results of operation and prognoses, and the progress of disease without surgical correction.
Methods
: Retrospective studies were performed on eleven CMS patients of less than 2 years of age admitted to Sejong General Hospital between Jan. 1989 and Aug. 1999.
Results
: The surgeries were performed on 9 out of 11 enrolled patients. The median age was 8(3-20) months and the median weight was 5(4-9)kg. The mitral valves of the patients were classified anatomically as supramitral ring(4), parachute mitral valve(3), “typical” symmetric hypoplastic mitral valve(2) and asymmetric hypoplastic mitral valve(2). Three patients died after the surgical correction. Among them, fibroelastosis of left ventricle was found during the surgery in two cases, and the other case was considered to be in Eisenmenger state.
5. Reoperations were performed on 3 out of 6 surviving patients. While one case was an early reoperation, two cases were late ones.
Conclusion
: The patients with severe CMS under the age of two can be surgically corrected with an acceptable success rate. Poor results were observed, however, if the decisions for surgical intervention were delayed. |
| Key Words:
Congenital mitral stenosis |
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