| A Case of Tuberous Sclerosis Complex Developing with Subependymal Giant-Cell Astrocytoma and Hydrocephalus |
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Ki Hyun Chung, Wan Sub Kim |
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Department of Pediatrics, Presbyterian Medical Center, Chonju, Korea |
| 뇌수두증과 상의하 거대세포 성상세포증이 동반된 결절성 경화증 1례 |
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정기현, 김완섭 |
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전주예수병원 소아과 |
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| Abstract |
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The subependymal giant-cell astrocytoma, a key feature of the tuberous sclerosis complex, has been reported in patients without obvious features of this condition. The tumor is a rare cerebral glioma that characteristically arise in the wall of lateral ventricle and as an intraventricular mass, causing hydrocephalus by obstruction of the foramen of Monro. We experienced a case of tuberous sclerosis in 9-year-old male patient who presented typical clinical manifestations and cortical tuber, subependymal giant-cell astrocytoma developing with hydrocephalus.
Diagnosis was confirmed by brain CT and MRI. We applied surgical resection to remove the mass. Brief review and related literatures were also presented. |
| Key Words:
Subependymal giant-cell astrocytoma, Tuberous Sclerosis Complex |
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